A unique case of a meningeal melanocytoma located in the pineal region is p
resented. This 48-year-old man presented with a round pineal region tumor t
hat caused triventricular hydrocephalus and exhibited slow clinical progres
sion. During surgery a black encapsulated tumor was found and totally remov
ed. On histopathological examination, the tumor proved to be a meningeal me
lanocytoma. in this report cell culture data are presented and the relevant
literature is reviewed. The problems of histopathological diagnosis and ma
nagement of patients with melanocytomas are also discussed.