Gorham syndrome: anaesthetic management

Gorham syndrome is a rare chronic disease of children and young adults, fea turing massive osteolysis with pathological fractures and complicated by re spiratory and neurological deficits. To date, 175 cases have been reported in the literature but information on anaesthetic management is sparse. We p resent a child with Gorham syndrome who underwent urgent surgical medullary decompression and who subsequently developed bilateral pleural effusions.