Extraskeletal myxoid chondrosarcoma (EMC) is an intriguing entity with a br
oad morphologic spectrum that overlaps features found in other benign and m
alignant mesenchymal tumors. This phenotypic plasticity should be known to
avoid erroneous diagnosis. The identification of older age, larger tumor si
ze, proximal tumor location, and metastatic disease as independent adverse
predictors of survival is useful in achieving optimal treatment and follow-
up in high-risk patients.