Megaduodenum in chronic intestinal pseudo-obstruction: management by duodenectomy-duodenoplasty.

Background - Surgical management of primitive chronic intestinal pseudo-obs truction involving the duodenum (megaduodenum) is on uncommon but still dif ficult problem. Patients and methods - Six patients who experienced severe symptoms were ma naged by on original surgical procedure including partial duodenal resectio n and reconstruction of a duodenal tract using large duodenal anastomosis ( duodenectomy-duodenoplasty). Results - There was no postoperative complication. All preoperative symptom s completely regressed in all but one patient who had previously undergone a vagotomy and experienced transient early post-operative gastric stasis. W ith a median follow-up of 6 years (range 4-9), all patients had good functi onal results without any evidence of other motility disorders. The mean wei ght gain was 10 kg (range 7-15). Conclusions - Duodenectomy-duodenoplasty is a safe procedure resulting in e fficient symptom relief in patients suffering from megaduodenum.