Primary pericardial disease is rare in children. The clinical features usua
lly reflect limited venous return and cardiac output. Tuberculous pericardi
tis is the leading cause of pericardial disease in developing nations. A de
finitive diagnosis in children is frequently difficult and the manifestatio
ns are protean. We report a 10-month-old. girl with fibrinofibrous pericard
itis that manifested as constrictive pericarditis with prolonged fever, hep
atomegaly, edema, and poor appetite. Echocardiography shelved a solid mass
that originated from the thickened pericardium and compressed the whole hea
rt. In contrast, computed tomography revealed pericardial thickening with f
luid collection. The symptoms and signs dramatically improved after surgica
l pericardiectomy. Pathologic analysis confirmed the diagnosis of tuberculo
us fibrinofibrous pericarditis. The patient received a 1-year course of ant
ituberculosis therapy and has remained symptom free for 2 years. We suggest
that a discrepancy between echocardiography and computed tomography (CT) f
indings might indicate a diagnosis of fibrinofibrous pericarditis.