An unusual. case of acquired development of anomalous intrapulmonary venous
connection with pulmonary venous stenosis is presented. Appearances on a c
hest radiograph resembled the "scimitar" sign in a patient with previous su
rgery for partial anomalous pulmonary venous return. Spiral CT and pulmonar
y arteriography showed stenosis of the right upper pulmonary vein and an an
omalous intrapulmonary venous connection between the right upper pulmonary
vein and the right lower pulmonary vein. We consider the slow progression o
f pulmonary vein stenosis led to anomalous intrapulmonary venous connection
as an intrapulmonary collateral.