Aggressive angiomyxoma of the vulva and perineum: A case report and reviewof the literature

Aggressive angiomyxoma is a rare locally aggressive mesenchymal tumor that preferentially involves the pelvic and perineal region in females. The peak incidence is in the fourth decade of life. Wide local excision is the trea tment of choice. The tumor has a strong propensity for local recurrence but distant metastasis has not been reported. Recurrence can develop up to 14 years after initial resection and long-term follow-up is recommended. The t umors can express estrogen and progesterone receptors but hormonal therapy is unproved. We describe a patient with aggressive angiomyxoma and review t he literature.