Medulloepithelioma of the ciliary body. A case report

Medulloepithelioma of the ciliary body is an uncommon intraocular tumor occ urring during the first year of life. Malignant degeneration may occur. We report the case of a 4-year-old child who presented medulloepithelioma of t he left eye disclosed by oesotropia at 2 years of age. Clinically, there wa s oesotropia, positive light perception and cataract with vascular membrane spreading to the nasal side of the irido-corneal angle. CT scan and ultras ound B revealed a ciliary body tumor involving the sclera and orbital fat. After exenteration, the pathology study reported malignant medulloepithelio ma of the ciliary body with scleral extension. No local recurrence or metas tasis has been observed at 8 months follow-up. We discuss the clinical, rad iological and therapeutic features of this uncommon tumor.