R. Jarrahy et al., Congenital teratoma of the oropharyngeal cavity with intracranial extension: Case report and literature review, J CRANIOF S, 11(2), 2000, pp. 106-112
Congenital teratoma of the oropharyngeal cavity is a unique clinical entity
that poses immediate threats to the neonate in the postpartum period. Esta
blishment of a secure airway is a primary goal after delivery; complete sur
gical resection is the subsequent guiding principle of management. Even mor
e rare than teratomas confined to the oropharynx are tumors that extend int
o the intracranial cavity during development. Descriptions of these lesions
in the medical literature are uncommon. In the majority of these reports,
the tumors are associated with stillbirth, perinatal death, or significant
morbidity after attempted resection. We present the rare case of a patient
with congenital oropharyngeal teratoma with intracranial extension who has
demonstrated long-term survival without any neurological or functional defi
cits. A unique delayed staged approach to resection of the extracranial and
intracranial components of the tumor is described.