Benign lymphangioendothelioma of the thigh simulating a low-grade angiosarcoma

Benign lymphangioendothelioma (BL) is a rare vascular neoplasm that can his topathologically mimic a low-grade angiosarcoma or the patch stage of Kapos i sarcoma. We report on the case of a 49-year-old man with a benign lymphan gioendothelioma on the right thigh that evolved on a vascular birthmark aft er a trauma. Because of constant pain and the slow but progressive growth o f the lesion, we decided to excise the tumor. Three stages of surgery were needed to obtain negative margins. We review the reports of BL to date, wit h special attention to those that developed after trauma and those that had a preexistent vascular lesion, and expound on the histopathologic differen tial diagnosis with low-grade angiosarcoma.