J. Caird et al., March 2000: 5 month old boy with occipital bone mass - Diagnosis - Melanotic neuroectodermal tumour of infancy., BRAIN PATH, 10(2), 2000, pp. 317
The March COM: A 5 month old boy was found by his mother to have a bony mas
s behind the left ear which extended intracranially on MRI scan. At surgery
it was entirely extradural in location. Microscopically, a biphasic appear
ance consisting of large pigmented cells arranged into tubules and small no
npigmented basophilic veils arranged into nests gave rise to a diagnosis of
melanotic neuroectodermal tumour of infancy [MNETI]. One year after a wide
local excision the patient is tumor-free and developing normally. The prog
nosis for MNETI in general is excellent with no requirement for additional
radiotherapy or chemotherapy.