Sjogren's syndrome with primary biliary cirrhosis, complicated by transverse myelitis and malignant lymphoma

A 53-year-old woman with Sjogren's syndrome (SS) and primary biliary cirrho sis (PBC) complicated by transverse myelitis (TM) and malignant lymphoma (M L) is reported. TM has been described only in seven cases of primary SS, in cluding three with PBC and Four without PBC, The features of SS associated with PBC and complicated by TM were less typical compared with those seen i n SS without PBC complicated by Thf, This case is the first report of a cas e with SS, PBC, TM and ML. SS in association with PBC is, in general, overl ooked, but such cases must be investigated with great caution for extraglan dular complications.