Background: Low anorectal malformations are considered to be a benign type
of anorectal malformations. Their treatment is simple in the neonatal perio
d and gives good results as far continence is concerned.
Methods: We studied a group of 55 boys with low anorectal malformations whi
ch had been surgically treated between the 1st January 1975 and the 31st De
cember 1992. We studied the initial treatment and the associated anomalies.
5 patients have died. 27 were seen for an interview and a clinical examina
tion. Extra investigations (anorectal manometry or electromyography of exte
rnal sphincter) were only offered to consenting patients with an ongoing pr
oblem.
Results: 3 to 20 years had passed since their operations. Associated anomal
ies had been found in 11 children. The initial treatment was a perineal pro
cedure in 20 cases and a colostomy In 8 cases. Dilatations were carried out
on 11 children. Faecal and urinary continence had been acquired before 30
months of age. 13 children (48%) had problems of soiling and/or chronic con
stipation. There was no difference between these children and the 14 contin
ent ones regarding the type of malformation, the initial treatment and the
follow-up. Anorectal manometry (performed on 9 cases) showed 4 anorectal dy
ssynergies. It was normal in 3 cases. The Recto Anal Inhibitory Reflex was
always present.
Conclusion: Problems of continence are not rare in the evolution of low ano
rectal malformations. We suggest therefore a longterm clinical follow-up fo
r those children, with one anorectal manometry control being performed afte
r continence is acquired.