A. Delarue et al., Delayed cure of an omphalocele requiring abdominosternoplasty, right hepatectomy and partial splenectomy, EUR J PED S, 10(1), 2000, pp. 58-61
A large ventral hernia resulting from the primary treatment of an omphaloce
le according to the Gross technique was repaired at age 16. The girl presen
ted with extra-abdominal development of the liver and the spleen along with
hypotrophy of the abdominal and thoracic cavities. The operation included
enlargement sternoplasty, liver and spleen-size reduction and prosthetic ab
dominal closure. The cosmetic and functional results are good and stable on
7-year follow-up. Surgical issues and blood transfusion policy are discuss
ed. A multi-disciplinary pediatric surgical approach is advocated.