Endovascular treatment of an unusual arterioportal fistula caused by the rupture of a giant hepatic artery aneurysm into the superior mesenteric veinin Behcet disease

BEHCET disease is a rare, chronic, multisystem disorder with a variety of s ymptoms. It most often affects men between the ages of 20 and 40 years. Alt hough it occurs worldwide, it occurs particularly often in Mediterranean co untries, the Middle East, and Japan. The etiology of Behcet disease remains obscure. It is considered an autoimmune disease because of the common deno minator of vasculitis in most patients. Histologic study of the affected ve ssels shows leukocytoclastic vasculitis, which leads to thrombosis, obstruc tion, aneurysm formation, and rupture of vessels. Arteries, capillaries, an d veins of various sizes are affected. Behcet aneurysms may involve the who le arterial tree (1). We report a case of arterioportal fistula in a patient with Behcet disease, which resulted from spontaneous rupture of a giant hepatic artery aneurysm into the superior mesenteric vein (SMV).