MRI appearances of hip abnormalities in mucolipidosis, type III

Mucolipidosis type III (ML-III) is a lysosomal storage disease often presen ting with joint involvement. We report the MRI appearance of the hips in tw o siblings with ML-III showing abnormal signal intensity within the hips wi th increased synovial thickness, Although the etiology is uncertain this ma y reflect a fibrous response to ML-III.