To our knowledge, only 3 histopathologically proved cases of multicent
ric eighth cranial nerve schwannoma have been described in the literat
ure since 1981. We describe a patient with 2 isolated eighth cranial n
erve schwannomas arising separately from the left cochlea and internal
auditory canal. These 2 tumors were diagnosed using magnetic resonanc
e imaging prior to resection, and the diagnosis was further confirmed
by intraoperative findings and histopathologic analysis. The genetic m
olecular basis and clinical features of this rare tumor have been over
looked. The value of the transotic approach for total tumor removal is
emphasized.