Bilateral hip arthroplasty for ochronotic arthropathy

Ochronosis is a musculoskeletal manifestation of alkaptonuria, a rare hered itary metabolic disorder characterised by the absence of the enzyme homogen tisic acid oxidase and associated with various systemic abnormalities relat ed to the deposition of homogentisic acid pigment (ochronotic pigment). In this report, we describe a 53-year-old, HLA-B27(+) woman with ochronotic ar thropathy. In addition to the typical clinical features of the disorder, sh e had bilateral hip involvement, which was improved by cementless total hip prosthesis.