Coincidence of multiple, disseminated, tardive-eruptive blue nevi with cutis marmorata teleangiectatica congenita

A 71-year-old woman reported a slow progression of multiple bluish dark asy mptomatic macules and papules on the pretibial region of both lower legs fo r over 30 years. At birth a left-sided hypoplasia of the leg including the buttock accompanied by a connatal vascular nevus had been diagnosed. The ip silateral deep veins of the pelvis and leg had a normal anlage. Histopathol ogical examination revealed multiple blue nevi of the common type. The asso ciation of multiple blue nevi and cutis marmorata teleangiectatica congenit a with limb hypoplasia has not previously been reported and is discussed in this paper. One could speculate whether these symptoms represent a new syn drome, because by thorough examination the NAME syndrome could be ruled out . Copyright (C) 2000 S. Karger AG, Basel.