The clinical course, neuro-imaging features and neuropathologic findin
gs in a child with para-infectious acute cerebellar swelling are descr
ibed, Reversible transtentorial and transforaminal herniations occurre
d and required emergency posterior fossa decompression with external v
entricular drainage. Neuropathologic examination of a cerebellar biops
y demonstrated a subacute pathogen-free cerebellitis. Following neuros
urgical intervention and steroid therapy, symptoms and signs resolved
and the patient is well 3 years later, Acute para-infectious cerebella
r swelling is potentially fatal unless recognised and treated early in
its evolution.