Spontaneous dissection of the internal carotid artery is typically associat
ed with cerebral vascular infarction along the anterior and middle cerebral
distribution, whereas occipital infarction is usually related to posterior
circulation abnormalities. Hemianopsia with occipital infarction related t
o carotid artery dissection has therefore rarely been reported. A 40-year-o
ld woman in whom acute-onset hemianopsia developed, related to occipital in
farction secondary to internal artery dissection, is described. This atypic
al association is explained by anatomic variations of the posterior part of
the circle of Willis. Neuroimages showed occipital infarction related to i
nternal carotid artery dissection associated with hypoplasia of the proxima
l portion of the cerebral posterior artery (P1). The anatomic correlation o
f this atypical association and a review of the literature are presented.