KID syndrome associated with features of ichthyosis hystrix

Keratitis-ichthyosis-deafness (KID) syndrome is a congenital ectodermal dis order causing erythrokeratoderma, vascularizing keratitis, and neurosensory deafness, Ichthyosis hystrix is a rare cutaneous disease characterized by well-demarcated, spiky, verrucous, linear plaques that is believed to be a clinical and pathologic chimera of two autosomal dominant diseases: epiderm al nevus and epidermolytic hyperkeratosis. We present a patient with the cl assic triad of KID syndrome with clinical and histologic features of ichthy osis hystrix, This case demonstrates that KID syndrome comprises a spectrum of ectodermal disorders which may include diseases such as hystrix ichthyo sis and deafness (HID) syndrome.