Laser surgery in a patient with Romano-Ward (long QT) syndrome and an automatic implantable cardioverter defibrillator

A 48-year-old women with Romano-Ward syndrome (a hereditary long QT syndrom e), asthma and an automatic implantable cardioverter defibrillator presente d for laser surgery for debulking of a massive nasopharyngeal tumour prior to radiotherapy. Automatic implantable cardioverter defibrillators have onl y relatively recently been used to treat patients with the long QT syndrome and are indicated for the high-risk individual when conventional treatment has failed or when beta-blockers are contraindicated. If surgery requires the use of surgical diathermy, a cardiac technician must be present to deac tivate the defibrillator and external pacing electrodes are sited on the ch est until the defibrillator can be reactivated. Radiotherapy requires both deactivation and shielding of the device.