CONGENITAL ORBITAL TERATOMA - A CLINICOPATHOLOGICAL CASE-REPORT

A 5-day-old infant boy tvas noted to have severe left proptosis at bir th. The left eye protruded superotemporally through the palpebral fiss ure and had exposure keratopathy. There was frank left afferent pupill ary defect. Computerized tomography (CT) showed a left orbital soft ti ssue mass with foci of calcification. Magnetic resonance imaging (MRI) studies revealed a left orbital mass with solid and cystic portions w ithout intracranial extension. As the eye tvas considered to be nonsal vagable, a lid-sparing type, modified exenteration was performed. Hist opathologic examination demonstrated various mature tissues of all thr ee embryonic germinal cell lines. This case represents one of the rare examples of true congenital orbital teratoma, which is an uncommon ca use of hideous proptosis In the neonate. MRI may prove useful in diffe rentiating this tumor from more common conditions.