Background. Absence of the portal bifurcation is exceptional and characteri
zed by an absent extrahepatic portal vein bifurcation, the right portal vei
n only being at the porta hepatis. There is no extraparenchymal left portal
vein. This may represent a problem in liver splitting, reduction, and livi
ng related transplantation.
Method A case was encountered during reduction of a cadaveric liver allogra
ft to a left lateral segmental graft from a 40-kg cadaveric donor to a 15-k
g recipient. The portal venous inflow was reconstructed with a vein graft v
ia a novel extrahilar approach to the left portal vein at the umbilical fis
sure.
Results. This graft was used successfully in a 3-year-old child requiring t
ransplantation for a failed Kasai operation for extrahepatic biliary atresi
a. The child is now well, 1 year posttransplant, after an uneventful postop
erative course with good portal flow within the graft.
Conclusion. The situation of an absent left portal vein extrahepatic course
should not preclude splitting or reduction procedures. The innovative tech
nical solution, we propose, should add to the armamentarium of the liver tr
ansplant surgeon contemplating a left lateral segmental graft for the paedi
atric liver transplant recipient.