Intra-abdominal desmoplastic small round cell tumor in a 68-year-old female

Background: Desmoplastic small round cell tumor (DSRCT) of the peritoneum t ypically occurs in young adults. The mean age of females with DSRCT is 20 y ears. We describe a DSRCT with an unusual age of presentation mimicking a m etastatic ovarian neoplasm. Case: A 68-year-old para 4 female presented with abdominal enlargement. Lap aratomy showed multiple tumor nodules attached to the peritoneal surface. T he tumor was debulked. The histological findings were characteristic for DS RCT Adjuvantly the patient received cytotoxic chemotherapy but died of recu rrent disease 3 months after initial diagnosis. Conclusion: DSRCT should be added to the differential diagnosis of unusual gynecologic malignancies in elderly as well as younger females. Identificat ion of DSRCT is important because it can be confused with primary ovarian n eoplasms.