Congenital and childhood dermatofibrosarcoma protuberans: A case report and review of the literature

Dermatofibrosarcoma protuberans (DFSP) occurs most commonly on the trunk, a ffects all races, and often develops between the second and fifth decades o f life. It is uncommon in childhood and is sometimes mistaken for a vascula r lesion, as it often presence as a blue macule or small nodule. Review of the English literature revealed approximately 152 cases of DFSP developing before 16 years of age and only 19 claimed congenital cases. A case of cong enital dermatofibrosarcoma protuberans is presented with a literature revie w and discussion of congenital and childhood presentations of the tumor.