Immunoglobulin related amyloidosis presenting as isolated lymph node and pulmonary involvement

Here we present an unusual case of a 53-year old patient presenting AL-kapp a amyloidosis with diffuse-type amyloidosis of lungs, lymph nodes and pleur a. The underlying pathology was a B-cell immunoglobulin-secreting non-Hodgk in lymphoma, as proven by the presence of a monoclonal B-cell population in the bone marrow. Diffuse parenchymal infiltration of the lungs is extremel y rare in non-systemic amyloidosis, with only 4 previous cases having been reported in the English literature.