Carcinoid tumors are endocrine malignancies that are often associated with
a characteristic syndrome, the malignant carcinoid syndrome, which is most
common in patients with small bowel tumors and liver metastases. In the rar
e instances when the syndrome is present without liver metastases the prima
ry tumor is usually localized to the bronchus or ovary and secretes hormone
s directly into the systemic circulation. About two thirds of patients with
carcinoid syndrome have evidence of carcinoid heart disease.
We report on a case of a primary ovarian carcinoid tumor with an unusual cl
inical presentation.