A 9-month old boy with a primary cystic lymphangioma of the right kidn
ey is reported. The clinical and radiological features favored a malig
nant tumor. Histology revealed the lesion to be a lymphangioma; the di
agnosis was confirmed by immunohistochemistry and chemical analysis of
the intracystic fluid. Lymphangiomas of the kidney are rare in adults
; they are even rarer in infants and children. Nevertheless, renal lym
phangiomas should be considered in the differential diagnosis of multi
cystic, unilateral renal masses, independent of the age of the patient
.