A 61-year-old woman, who was diagnosed in 1982 as having polycythemia vera,
was admitted to our hospital in July 1998 because of a splenic tumor in an
enlarged spleen due to myelofibrosis. As it was difficult to identify the
etiology of the splenic tumor, partial splenectomy was carried out. The res
ected tumor proved to be an extremely proliferative lesion as the result of
extramedullary hematopoiesis, Since it is difficult to diagnose the etiolo
gy of splenic tumor, the collection and analysis of reports of relevant cas
es may well facilitate diagnosis.