Granulocytic sarcomas are rare extramedullary tumors of malignant myeloid p
recursor cells. Exceedingly rare in childhood, it commonly involves skin, l
ymph nodes, bone, and the spine. Ovarian involvement is rare, it can arise
de novo, precede the development of acute nonlymphocytic leukemia, or be th
e sole manifestation of relapse. We describe a 26-year-old woman with granu
locytic sarcoma of the ovary without any hematologic disorder.