B. Roques et al., Intra-abdominal desmoplastic small round-cell tumors. An entity among peritoneal carcinomatosis in young adults, GASTRO CL B, 24(3), 2000, pp. 359-360
Desmoplastic small round-cell tumors in young adults were first described i
n 1989. They may be revealed by an abdominal mass or a peritoneal carcinoma
tosis. The diagnosis and the initial treatment are based on debulking surge
ry. Chemotherapy using doxorubicin, ifosfamide, etoposide and cisplatin can
then be proposed. Despite some initial chemosensitivity prognosis remains
poor.