Unilateral macular retinoschisis with stellate foveal appearance in two females with myopia

Stellate foveal retinoschisis is considered the hallmark of X-linked retino schisis. We describe the finding of unilateral retinoschisis with stellate foveal appearance in 2 females with myopia who had no evidence of familial disease. Optical coherence tomography (OCT) and fluorescein angiography wer e obtained in both cases. Neither patient had a family history of low visio n, night blindness, or retinal detachment. Visual acuity in the affected ey es was 20/50 and 20/25, respectively. Both fellow eyes had normal fundi, ex cept for mild myopic changes. With OCT, widespread retinal splitting was de tected at the posterior pole in the affected eyes, whereas the fellow eyes were normal. In one case, OCT showed that foveal retinoschisis represented the macular involvement of a flat inferior retinoschisis, although this was not clinically apparent. Macular retinoschisis with stellate foveal appear ance may rarely be associated with pathologic myopia. OCT was useful to est ablish the true extension of these macular changes.