CONGENITAL HEMANGIOPERICYTOMA INFANTILE MYOFIBROMATOSIS - RADICAL SURGERY VERSUS A CONSERVATIVE WAIT AND SEE APPROACH

Infantile/congenital hemangiopericytoma, although sharing many similar histological features with adult hemangiopericytoma, has a much bette r prognosis. Nevertheless, most cases described in the literature were pursued by radical surgery with or without adjuvant chemotherapy. We describe a neonate who presented with a huge mass in the right gluteus , 6 x 5 x 4 cm, and a small ventral abdominal mass. The masses were co nfirmed on biopsy according to light microscopy, immunohistochemistry, and electron microscopy as congenital hemangiopericytoma. They shrank spontaneously within 2 weeks and vanished within 2 months. We present a hypothesis that masses appearing in the neonatal period with this h istology and with no life-endangering pressure on vital organs should routinely be dealt with conservatively.