Background: Sigmoid volvulus is an exceptionally rare and potentially life-
threatening condition in the pediatric age group.
Study Design: We report our experience with three children treated for sigm
oid volvulus and review the cases reported in the medical literature since
1940.
Results: Since 1940, 63 cases of sigmoid volvulus in children (including th
is series) have been reported. The median age was 7 years and the male to f
emale ratio was 3.5:1. Two distinct presentations (acute and recurrent) wer
e identified. Abdominal symptoms dominated the clinical picture. Barium ene
mas either confirmed or were highly suggestive of sigmoid volvulus. Reducti
on by barium enema was successful in 77% (10 of 13) of the attempts. Forty-
nine patients underwent operative treatment, with sigmoidectomy (with or wi
thout primary anastomosis) being the most common. The overall mortality rat
e was 6%, operative mortality was 8.1%, and neonatal mortality was 14%. Ass
ociated conditions were frequent. Particular emphasis should be placed on r
uling out Hirschsprung's disease (present in 11 of 63 patients).
Conclusions: Sigmoid volvulus remains a rare occurrence in children, but it
should be included in the differential diagnosis of pain in children when
colonic distention is present. An algorithm for treatment is proposed. (J A
m Coll Surg 2000;190:717-723. (C) 2000 by the American College of Surgeons)
.