A patient with Ehlers-Danlos syndrome type IV had a celiac artery aneurysm.
There are only nine previously published cases of visceral artery aneurysm
s in this condition, and surgical management was used in only four of them.
This is, are believe, the first published report of a successfully treated
celiac artery aneurysm in this condition in which the hazards of treatment
and our rationale are explained. The literature of this rare problem is al
so reviewed.