Bronchiolitis obliterans organizing pneumonia: A distinct pulmonary complication in cystic fibrosis

pneumonia in cystic fibrosis has hitherto been considered a nonspecific rep arative process. We report on an adult patient with cystic fibrosis and his tologically proven bronchiolitis obliterans organizing pneumonia, who exper ienced sustained clinical improvement under corticosteroid therapy. This ca se suggests that bronchiolitis obliterans organizing pneumonia may be a dis tinct pulmonary complication in cystic fibrosis and improve with specific t herapy. Copyright (C) 2000 S. Karger AG, Basel.