Multiple odontogenic keratocysts in mental retardation-overgrowth (Simpson-Golabi-Behmel) syndrome

Authors
Krimmel, M Reinert, S
Citation
M. Krimmel et S. Reinert, Multiple odontogenic keratocysts in mental retardation-overgrowth (Simpson-Golabi-Behmel) syndrome, BR J ORAL M, 38(3), 2000, pp. 221-223
Citations number
8
Categorie Soggetti
Dentistry/Oral Surgery & Medicine
Journal title
BRITISH JOURNAL OF ORAL & MAXILLOFACIAL SURGERY
ISSN journal
02664356 → ACNP
Volume
38
Issue
3
Year of publication
2000
Pages
221 - 223
Database
ISI
SICI code
0266-4356(200006)38:3<221:MOKIMR>2.0.ZU;2-C
Abstract
We report on a 10-year-old boy with mental retardation-overgrowth (Simpson- Golabi-Behmel) syndrome. The child had the typical clinical features includ ing, postnatal overgrowth, mental retardation, and a characteristic facial appearance. He was admitted for treatment of multiple mandibular and maxill ary cysts. Histopathological examination of the cyst tissue showed keratini zed epithelium. Odontogenic keratocysts may have to be added to the typical features of this syndrome.