Conventional aortoplasty procedures do not fully restore the normal anatomy
in supra-valvular aortic stenosis (SVAS), which involves the sinus rim as
well as the aortic cusps. A tri-sinus repair of this condition is proposed
to restore the three intercommissural distances to normal and adequately re
place the tissue loss of the sinuses, for a symmetrical reconstruction of t
he aortic root. Two patients, aged 3 and 11 years, with localized type of s
upra-valvular aortic stenosis were operated, in May 1994 and February 1996.
The aortic stenosing ring was opened up at three points, by extending the
incision into all the three sinuses, and the defect was repaired with in si
tu autologous pericardium, in a tri-foliate fashion. This repair achieved a
symmetrical reconstruction of the aortic root and the systolic pressure gr
adient was completely abolished. Postoperative aortic root angiogram, in th
e older of the two patients, revealed a normal appearing aortic root. The p
atients have been followed-up for 51 months and 30 months respectively. Ech
ocardiography showed competent aortic valves in both the patients without a
ny systolic gradient across the aortic valve, A tri-sinus repair of the aor
ta in SVAS results in a symmetrical reconstruction of the aortic root by re
storing the normal intercommissural distances of all the three cusps. It al
so abolishes the systolic pressure gradient. Autologous untreated pericardi
um lends itself easily for tailoring into a tri-foliate patch.