Objective: The pathophysiology of double elevator palsy is poorly unde
rstood. We assessed two patients with this condition using magnetic re
sonance imaging (MRI) to evaluate the appearance of the extraocular mu
scles. Design: Cross-sectional study. Setting: Radiology department of
a university-affiliate hospital in London, Ont. Patients: Two patient
s from a private ophthalmology practice who had undergone complete tra
nspositions of the horizontal rectus muscles to treat hypotropia assoc
iated With double elevator palsy, Intervention: MRI. A volume scanning
technique was used to obtain maximum information about the muscles. O
utcome measure: Appearance of the extraocular muscles. Results: In bat
h patients MRI showed decreased volume of the superior rectus muscle o
n the affected side. the other rectus muscles were normal. this sugges
ted either congenital hypoplasia or paresis of the involved superior r
ectus muscle. In addition, the lull tendon transpositions of the media
l and lateral recti did nor appreciably change the middle and deep orb
ital pathways of the transposed horizontal rectus muscles, Conclusions
: MR1 may be a useful adjunct to saccadic velocity assessments in diff
erentiating between primary inferior rectus restriction, primary super
ior rectus paresis and congenital supranuclear elevator deficiency.