BACKGROUND: The operations with proven effects on survival in Budd-Chiari s
yndrome are shunt operations and liver transplantation.
PATIENTS AND METHODS: Between 1993 and 1999 (June), 13 cases of Budd-Chiari
syndrome have been treated surgically. Four cases had concomitant thrombos
is of the inferior vena cava; the others had marked narrowing of the lumen
due to the enlarged caudate lobe. Mesoatrial (n = 12) or mesosuperior vena
caval (n = 1) shunts were constructed with ringed polytetrafluoroethylene g
rafts.
RESULTS: The median portal pressure fell from 45 (range 32 to 55) to 20 (ra
nge 11 to 27) cm H2O (P <0.001). Two patients died in the early postoperati
ve period. One patient who did not comply with anticoagulant treatment had
a shunt thrombosis in the second postoperative year. The other 10 patients
are alive without problems during a median 42 (range 1 to 76) months of fol
low-up.
CONCLUSION: Mesoatrial shunt with a ringed polytetrafluoroethylene graft is
effective in Budd-Chiari syndrome cases with thrombosis or significant ste
nosis in the inferior vena cava. Am J Surg. 2000;179:304-308. (C) 2000 by E
xcerpta Medica, Inc.