Leptomeningeal metastasis of low-grade gliomas in children has been documen
ted in several series, both at the time of diagnosis and at relapse. The au
thors report a unique case of chiasmatic low-grade astrocytoma presenting w
ith signs and symptoms related to the metastatic site rather than the prima
ry site. In this respect, the possibility of appearance of symptoms and sig
ns related to leptomeningeal dissemination preceding the signs and symptoms
belonging to the primary site should be considered in this type of benign
rumours.