This study presents a combined case series of chordomas from two Canadian i
nstitutes. Twenty-seven patients were identified for the period 1954-1998.
Management issues with regard to diagnostic pitfalls, selection of charged
particle treatment and retreatment of recurrences are discussed, The diagno
sis of early stage chordoma requires a high index of suspicion. One patient
in the series presented with hoarseness and is described in detail. The di
agnosis was made coincidentally by a computed tomographic scan of the head,
performed after a motor vehicle accident. The planning of both surgery and
radiotherapy was optimized by using magnetic resonance imaging. A review o
f the literature supports the use of a combined surgical and radiotherapeut
ic approach.