The purpose of this study is to analyze the characteristics of patients pre
senting with pelvic mass and diagnosed with sarcoma of the ileum at laparot
omy. A retrospective review of patients' files and pathology reports was ma
de. Five cases of leiomyosarcoma of the ileum constituted 0.7% of 728 new c
ases with a final pathologic diagnosis of gynecologic or other pelvic malig
nancy. The median age of the 5 patients was 58 years. All patients presente
d with a pelvic mass and underwent ileal resection with end-to-end anastomo
sis. Two patients with disseminated tumors at the time of initial surgery d
ied of their disease, and those with early-stage tumors remained alive and
tumor free. It is concluded that ileal leiomyosarcomas may show signs and s
ymptoms of ovarian carcinoma. Gynecologic oncologists should have an unders
tanding of these pathologic entities and their natural history and be ready
to perform the necessary surgical procedures for these small bowel tumors.