Narrow internal auditory canal (IAC) syndrome is a malformation of the temp
oral bone, that is defined as an IAC diameter of only 1-2 mm on high-resolu
tion computed tomographic scans (HRCT). This syndrome is known to be caused
by the absence (aplasia or hypoplasia) of the vestibulocochlear nerve. We
present a case of unilateral narrow IAC syndrome which was diagnosed by HRC
T. The aplasia of the vestibulocochlear nerve was confirmed using parasigit
tal reconstruction magnetic resonance image (MRI). The IAC was composed of
two separate canals, one of which contained a facial nerve and the other wa
s empty with aplasia of the vestibulocochlear nerve.