Complete tracheal agenesis is a very rare congenital anomaly that is only c
ompatible with life in some cases with associated tracheo-oesophageal or br
oncho-oesophageal fistula. In most cases, concomitant congenital anomalies
of the heart, digestive tract or genitourinary tract are present. It should
be suspected in any neonate with a history of hydramnios, absent crying, r
espiratory distress and difficulty in intubation. The possibility for surgi
cal correction or palliation rests on the extent of atresia present. We pre
sent a case of complete tracheal agenesis without tracheo nor broncho-oesop
hageal fistula (type II by Floyd's classification) - the diagnosis of which
was prenatally suspected - and discuss the important features of the airwa
y management of this condition.