J. Shirani et al., TRANSIENT LOSS OF VISION AS THE PRESENTING SYMPTOM OF PAPILLARY FIBROELASTOMA OF AORTIC-VALVE, Cardiovascular pathology, 6(4), 1997, pp. 237-240
Cardiac papillary fibroelastomas are benign endocardial papillomas. Th
ey may arise from atrial or ventricular endocardium but most commonly
are located in cardiac valves. Their papillary structure, with loose,
friable projections, results in a high tendency for embolism. Turner f
ragments often embolize to the coronary, systemic, or cerebral arteria
l systems. Thus, acute myocardial infarction, cerebrovascular accident
, or peripheral arterial occlusion have resulted from these tumors. Re
tinal artery embolism is a rare complication of papillary fibroelastom
a, and only five such patients have been reported in the English-langu
age literature. We describe a 64-year-old woman who presented with tra
nsient painless loss of vision and was found to have a large papillary
fibroelastoma on the right coronary cusp of the aortic valve by trans
esophageal echocardiography. The tumor was success fully removed at su
rgery. (C) 1997 by Elsevier Science Inc.