Primary renal non-Hodgkin's lymphoma (NHL) is unusual, in contrast to the f
requent renal involvement in disseminated NHL. We report a case of follicul
ar lymphoma presenting initially as a renal mass. In the literature, twenty
-seven similar cases have been described since 1980. The median age at diag
nosis is 64 years with a male predominance. Clinical and radiological findi
ngs generally evoke renal carcinoma. Histologically, tumors are usually lar
ge B-cell lymphomas. The existence of renal non-Hodgkin lymphoma mimicking
renal carcinoma must be recognized. Such lymphomas can either be primitive
or be nodal with a renal presentation. Nephrectomy followed by chemotherapy
permits long disease free survival.