Nevoid basal cell carcinoma syndrome (NBCCS) is a hereditary disorder with
a predilection for numerous basal cell carcinomas in addition to odontogeni
c keratocysts, palmoplantar pitting, and skeletal malformations. NBCCS has
been associated with a number of benign and malignant neoplasms. We report
the first case of NBCCS in association with non-Hodgkin's lymphoma.